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Birthmarks and Vascular Anomalies Center
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Birthmarks and Vascular Anomalies Center
Klippel-Trenaunay Syndrome (KT)

KT is a syndrome of port wine stains, varicose veins, and bony or soft tissue overgrowth (when the affected area is larger than unaffected areas). The first signs of KT are on the skin and usually only on one extremity. The lymphatic vessesl are often involved which leads to swelling or lymphedema. The overgrowth of the affected limb can appear at birth or in the first few months of life.

Venous Malformation and Port Wine Satin in Klippel-Trenaunay Syndrome

The cause of KT is unknown. It affects more males than females. Other syndromes and anomalies may be associated with KT.

KT is diagnosed by history and exam by an experienced physician.

There is no cure for KT. Management includes regular visits with a doctor with clinical and radiographic measurements of the affected limb. MRI and Ultrasound/Doppler imaging are very useful for determining the depth and extent of the disorder. Orthopedic evaluation is very important for children with limb length differences.

Treatment is usually symptomatic and conservative. Treatment can include compression stockings or dJuly 14, 2006or "blebs" associated with KT.

 

Updated: November 30, 2007
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